CLEIDOCRANIAL DYSPLASIA

Authors

  • Ana Karine Farias Trindade
  • Maria Sueli Marques Soares
  • Cláudia Cazal Lira
  • Maria Luiza Anjos Pontual

Abstract

Cleidocranial Dysplasia is a disease caused by an autosomal dominant gene that presents with a skeletal dysplasia. Patients with the disease commonly present retention of primary teeth, impaction and delayed eruption of permanent teeth, and presence of supernumerary teeth. In this study the aim was to relate a clinical case of Cleidocranial Dysplasia and discuss the general aspects, clinical and radiographic signs of the mentioned Syndrome. The patient, a 14-year-old girl, resident in João Pessoa, PB, Brazil, presented at the Stomatology clinic of UFPB with the complaint of prolonged retention of primary teeth and delayed eruption of permanent teeth. On clinical and radiographic exam, the presence of typical characteristics of this dysplasia were observed, such as the permanence of various primary teeth, in addition to included and supernumerary teeth, hypoplasia of the claviculas and frontal and parietal sutures. After evaluation of all the clinical and radiographic characteristics presented by the patient the diagnosis of Cleidocranial Dysplasia was established. The patient was submitted to orthodontic evaluation and extraction of several primary teeth was requested in order to perform orthodontic traction afterwards.

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Published

2011-01-20

How to Cite

Trindade, A. K. F., Soares, M. S. M., Lira, C. C., & Pontual, M. L. A. (2011). CLEIDOCRANIAL DYSPLASIA. Revista Brasileira De Ciências Da Saúde, 14(2), 73–76. Retrieved from https://periodicos.ufpb.br/ojs/index.php/rbcs/article/view/7180

Issue

Vol. 14 No. 2 (2010)

Section

Report

License

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